Developing Treatment for Hereditary Neuromuscular Disease


 

Developing Treatment for Hereditary Neuromuscular Disease – Air date: Wednesday, November 02, 2011, 3:00:00 PM Timedisplayed is Eastern Time, Washington DC Local Category: Wednesday Afternoon Lectures Description: Several thousand human disease genes have been identified over the past 25 years. The challenge now is to convert what we know about the causes and mechanisms of hereditary diseases into safe and effective treatment. We are finally close to doing this for two pediatric neuromuscular diseases, Duchenne muscular dystrophy (DMD) and spinal muscular atrophy (SMA). DMD is characterized by progressive weakness due to muscle degeneration. The disease is caused by mutations in the muscle protein dystrophin. Most of the mutations are partial gene deletions that shift the translational reading frame of the mRNA, leading to a truncated and unstable protein. Approaches to treatment include enhancing muscle regeneration and replacing or correcting the gene at the DNA or mRNA level. Myostatin inhibition and drugs that promote read-through of mutations have shown benefit in animals but not yet in clinical trials. Gene replacement has low efficiency and may induce an immune response to dystrophin. Oligonucleotide therapy to induce exon skipping may be the most promising approach at present. The oligonucleotides target specific mutations at the mRNA level. Recent clinical studies have shown partial restoration of muscle dystrophin with local and systemic delivery, and international trials are in progress. SMA is the most common severe

 

Wal-Mart medical clinics trail CVS

Filed under: drug addiction treatment act of 2000

As key parts of the Patient Protection and Affordable Care Act start phasing in next year, some 30 million newly insured Americans will be looking for care amid a doctor shortage. Clinics, generally open after-hours and on weekends, minister to …
Read more on The News Journal

 

3444 Virginia gun purchases denied in 2012

Filed under: drug addiction treatment act of 2000

When adding denials for others prohibited from buying firearms, such as drug abusers, the mentally ill and domestic-assault offenders, Virginia's system has stopped 54,260 gun transactions over the past 24 years, records show. Virginia denied 3,444 …
Read more on The Daily Progress

 

Crain's week in news: Feb. 9-15

Filed under: drug addiction treatment act of 2000

Page, on the company board since 2000, will replace founder Merton Segal, who is retiring. Ford Motor Co. … Inc. that could be worth more than $ 300 million to develop small-molecule drugs to treat a range of immune-mediated disorders. Detroit-based …
Read more on Crain’s Detroit Business

 

The waking nightmare

Filed under: drug addiction treatment act of 2000

She had no way of knowing, or any reason for suspecting, that the anaesthetist was a drug addict who had injected the fentanyl into her bloodstream after first using the syringe on himself. In doing so, he … In Victoria's Supreme Court last week …
Read more on The Age